[Term] id: PR:Q10713-1 name: mitochondrial-processing peptidase subunit alpha isoform h1 (human) def: "A mitochondrial-processing peptidase subunit alpha (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q10713-1." [PRO:DNx, UniProtKB:Q10713] comment: Category=organism-sequence. synonym: "hPMPCA/iso:h1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q10713-1 is_a: PR:Q10713 ! mitochondrial-processing peptidase subunit alpha (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:P20069 name: mitochondrial-processing peptidase subunit alpha (rat) def: "A mitochondrial-processing peptidase subunit alpha that is encoded in the genome of rat." [PANTHER:PTHR11851:SF49, PRO:DNx] comment: Category=organism-gene. synonym: "Mppa" RELATED Gene-based [UniProtKB:P20069] synonym: "Pmpca" RELATED Gene-based [UniProtKB:P20069] synonym: "rPMPCA" EXACT PRO-short-label [PRO:DNx] synonym: "P-55 (rat)" EXACT [UniProtKB:P20069] synonym: "alpha-MPP (rat)" EXACT [UniProtKB:P20069] synonym: "inactive zinc metalloprotease alpha (rat)" EXACT [UniProtKB:P20069] xref: UniProtKB:P20069 intersection_of: only_in_taxon NCBITaxon:10116 ! Rattus norvegicus intersection_of: PR:000012911 ! mitochondrial-processing peptidase subunit alpha relationship: has_gene_template RGD:727897 ! Pmpca (rat) [Term] id: PR:Q10713-2 name: mitochondrial-processing peptidase subunit alpha isoform h2 (human) def: "A mitochondrial-processing peptidase subunit alpha (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q10713-2." [PRO:DNx, UniProtKB:Q10713] comment: Category=organism-sequence. synonym: "hPMPCA/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q10713-2 is_a: PR:Q10713 ! mitochondrial-processing peptidase subunit alpha (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q95XN2-1 name: mitochondrial-processing peptidase subunit alpha isoform a (worm) def: "A mitochondrial-processing peptidase subunit alpha (worm) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q95XN2-1." [PRO:DNx, UniProtKB:Q95XN2] comment: Category=organism-sequence. synonym: "PMPCA/iso:a (worm)" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q95XN2-1 is_a: PR:Q95XN2 ! mitochondrial-processing peptidase subunit alpha (worm) relationship: only_in_taxon NCBITaxon:6239 ! Caenorhabditis elegans [Term] id: PR:Q95XN2-2 name: mitochondrial-processing peptidase subunit alpha isoform b (worm) def: "A mitochondrial-processing peptidase subunit alpha (worm) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q95XN2-2." [PRO:DNx, UniProtKB:Q95XN2] comment: Category=organism-sequence. synonym: "PMPCA/iso:b (worm)" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q95XN2-2 is_a: PR:Q95XN2 ! mitochondrial-processing peptidase subunit alpha (worm) relationship: only_in_taxon NCBITaxon:6239 ! Caenorhabditis elegans [Term] id: PR:000012911 name: mitochondrial-processing peptidase subunit alpha def: "A protein that is a translation product of the human PMPCA gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "MPPA" RELATED Gene-based [] synonym: "P-55" EXACT [] synonym: "PMPCA" EXACT PRO-short-label [PRO:DNx] synonym: "INPP5E" RELATED Gene-based [] synonym: "KIAA0123" RELATED Gene-based [] synonym: "alpha-MPP" EXACT [] synonym: "inactive zinc metalloprotease alpha" EXACT [] is_a: PR:000000001 ! protein [Term] id: PR:P11914 name: mitochondrial-processing peptidase subunit alpha (yeast) def: "A mitochondrial-processing peptidase subunit alpha that is encoded in the genome of yeast." [OMA:P11914, PANTHER:PTHR11851:SF49, PRO:DNx] comment: Category=organism-gene. synonym: "MAS2" RELATED Gene-based [UniProtKB:P11914] synonym: "MIF2" RELATED Gene-based [UniProtKB:P11914] synonym: "yPMPCA" EXACT PRO-short-label [PRO:DNx] synonym: "YHR024C" RELATED Gene-based [UniProtKB:P11914] synonym: "MPP (yeast)" EXACT [UniProtKB:P11914] synonym: "alpha-MPP (yeast)" EXACT [UniProtKB:P11914] synonym: "matrix processing peptidase (yeast)" EXACT [UniProtKB:P11914] synonym: "mitochondrial assembly protein 2 (yeast)" EXACT [UniProtKB:P11914] synonym: "inactive zinc metalloprotease alpha (yeast)" EXACT [UniProtKB:P11914] synonym: "mitochondrial import function protein 2 (yeast)" EXACT [UniProtKB:P11914] xref: UniProtKB:P11914 intersection_of: only_in_taxon NCBITaxon:559292 ! Saccharomyces cerevisiae S288C intersection_of: PR:000012911 ! mitochondrial-processing peptidase subunit alpha relationship: has_gene_template SGD:S000001066 ! MAS2 (yeast) [Term] id: PR:Q95XN2 name: mitochondrial-processing peptidase subunit alpha (worm) def: "A mitochondrial-processing peptidase subunit alpha that is encoded in the genome of worm." [OMA:Q95XN2, PANTHER:PTHR11851:SF49, PRO:DNx] comment: Category=organism-gene. synonym: "mppa-1" RELATED Gene-based [UniProtKB:Q95XN2] synonym: "Y71G12B.24" RELATED Gene-based [UniProtKB:Q95XN2] synonym: "PMPCA (worm)" EXACT PRO-short-label [PRO:DNx] synonym: "alpha-MPP (worm)" EXACT [UniProtKB:Q95XN2] synonym: "inactive zinc metalloprotease mppa-1 (worm)" EXACT [UniProtKB:Q95XN2] xref: UniProtKB:Q95XN2 intersection_of: only_in_taxon NCBITaxon:6239 ! Caenorhabditis elegans intersection_of: PR:000012911 ! mitochondrial-processing peptidase subunit alpha relationship: has_gene_template WormBase:WBGene00022159 ! mppa-1 (worm) [Term] id: PR:000048830 name: mitochondrial-processing peptidase subunit alpha, transit peptide removed form (human) def: "A mitochondrial-processing peptidase subunit alpha (human) that has had the transit peptide removed. UniProtKB:Q10713, 34-525." [PRO:DNx, Reactome:R-HSA-1299450] comment: Category=organism-modification. synonym: "PRO_0000026767" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hPMPCA/TransPep-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:Q10713, 34-525" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-1299450 "PR:000048830 located_in GO:0005759" intersection_of: PR:Q10713 ! mitochondrial-processing peptidase subunit alpha (human) intersection_of: lacks_part SO:0000725 ! transit_peptide relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:000021020 name: mitochondrial-processing peptidase subunit alpha, transit peptide removed form def: "A mitochondrial-processing peptidase subunit alpha that has had the transit peptide removed." [PRO:DNx] comment: Category=modification. synonym: "PMPCA/TransPep-" EXACT PRO-short-label [PRO:DNx] intersection_of: PR:000012911 ! mitochondrial-processing peptidase subunit alpha intersection_of: lacks_part SO:0000725 ! transit_peptide [Term] id: PR:Q10713 name: mitochondrial-processing peptidase subunit alpha (human) def: "A mitochondrial-processing peptidase subunit alpha that is encoded in the genome of human." [PRO:DNx, UniProtKB:Q10713] comment: Category=organism-gene. synonym: "MPPA" RELATED Gene-based [UniProtKB:Q10713] synonym: "PMPCA" RELATED Gene-based [UniProtKB:Q10713] synonym: "INPP5E" RELATED Gene-based [UniProtKB:Q10713] synonym: "hPMPCA" EXACT PRO-short-label [PRO:DNx] synonym: "KIAA0123" RELATED Gene-based [UniProtKB:Q10713] synonym: "P-55 (human)" EXACT [UniProtKB:Q10713] synonym: "alpha-MPP (human)" EXACT [UniProtKB:Q10713] synonym: "inactive zinc metalloprotease alpha (human)" EXACT [UniProtKB:Q10713] xref: UniProtKB:Q10713 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000012911 ! mitochondrial-processing peptidase subunit alpha relationship: has_gene_template HGNC:18667 ! PMPCA (human) [Term] id: PR:O94745 name: probable mitochondrial-processing peptidase subunit alpha (Schizosaccharomyces pombe 972h-) def: "A mitochondrial-processing peptidase subunit alpha that is encoded in the genome of Schizosaccharomyces pombe 972h-." [OMA:O94745, PANTHER:PTHR11851:SF49, PRO:DNx] comment: Category=organism-gene. synonym: "mas2" RELATED Gene-based [UniProtKB:O94745] synonym: "SPBC18E5.12c" RELATED Gene-based [UniProtKB:O94745] synonym: "SPBC23G7.02c" RELATED Gene-based [UniProtKB:O94745] synonym: "Spom972h-PMPCA" EXACT PRO-short-label [PRO:DNx] synonym: "alpha-MPP (Schizosaccharomyces pombe 972h-)" EXACT [UniProtKB:O94745] synonym: "inactive zinc metalloprotease alpha (Schizosaccharomyces pombe 972h-)" EXACT [UniProtKB:O94745] xref: UniProtKB:O94745 intersection_of: only_in_taxon NCBITaxon:284812 ! Schizosaccharomyces pombe 972h- intersection_of: PR:000012911 ! mitochondrial-processing peptidase subunit alpha relationship: has_gene_template PomBase:SPBC18E5.12c ! mas2 (Schizosaccharomyces pombe) [Term] id: PR:Q9DC61 name: mitochondrial-processing peptidase subunit alpha (mouse) def: "A mitochondrial-processing peptidase subunit alpha that is encoded in the genome of mouse." [OMA:Q9DC61, PRO:DNx] comment: Category=organism-gene. synonym: "Pmpca" RELATED Gene-based [UniProtKB:Q9DC61] synonym: "Inpp5e" RELATED Gene-based [UniProtKB:Q9DC61] synonym: "mPMPCA" EXACT PRO-short-label [PRO:DNx] synonym: "P-55 (mouse)" EXACT [UniProtKB:Q9DC61] synonym: "alpha-MPP (mouse)" EXACT [UniProtKB:Q9DC61] synonym: "inactive zinc metalloprotease alpha (mouse)" EXACT [UniProtKB:Q9DC61] xref: UniProtKB:Q9DC61 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000012911 ! mitochondrial-processing peptidase subunit alpha relationship: has_gene_template MGI:1918568 ! Pmpca (mouse)