[Term] id: PR:000025741 name: isovaleryl-CoA dehydrogenase, mitochondrial isoform 1, transit peptide removed form def: "An isovaleryl-CoA dehydrogenase, mitochondrial isoform 1 that has been processed to remove the N-terminal mitochondrion transit peptide." [PMID:12665801, PRO:CNA] comment: Category=modification. synonym: "IVD/iso:1/TransPep-" EXACT PRO-short-label [PRO:DNx] intersection_of: PR:000025738 ! isovaleryl-CoA dehydrogenase, mitochondrial isoform 1 intersection_of: lacks_part SO:0000725 ! transit_peptide [Term] id: PR:000020356 name: isovaleryl-CoA dehydrogenase, mitochondrial, transit peptide removed form def: "An isovaleryl-CoA dehydrogenase, mitochondrial that has had the transit peptide removed." [PRO:DNx] comment: Category=modification. synonym: "IVD/TransPep-" EXACT PRO-short-label [PRO:DNx] intersection_of: PR:000009166 ! isovaleryl-CoA dehydrogenase, mitochondrial intersection_of: lacks_part SO:0000725 ! transit_peptide [Term] id: PR:000025742 name: isovaleryl-CoA dehydrogenase, mitochondrial isoform 1, transit peptide removed form (human) def: "An isovaleryl-CoA dehydrogenase, mitochondrial isoform 1, transit peptide removed form in human. UniProtKB:P26440-1, 33-426." [PMID:12665801, PRO:CNA, PRO:DAN] comment: Category=organism-modification. synonym: "PRO_0000000531" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hIVD/iso:1/TransPep-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:P26440-1, 33-426" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-70729 "PR:000025742 located_in GO:0005759" intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000025741 ! isovaleryl-CoA dehydrogenase, mitochondrial isoform 1, transit peptide removed form [Term] id: PR:000025738 name: isovaleryl-CoA dehydrogenase, mitochondrial isoform 1 def: "An isovaleryl-CoA dehydrogenase, mitochondrial that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q9JHI5-1 or a 1:1 ortholog thereof." [PRO:CNA] comment: Category=sequence. synonym: "IVD/iso:1" EXACT PRO-short-label [PRO:DNx] is_a: PR:000009166 ! isovaleryl-CoA dehydrogenase, mitochondrial [Term] id: PR:000009166 name: isovaleryl-CoA dehydrogenase, mitochondrial def: "A protein that is a translation product of the human IVD gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "IVD" EXACT PRO-short-label [PRO:DNx] is_a: PR:000000001 ! protein [Term] id: PR:P26440-1 name: isovaleryl-CoA dehydrogenase, mitochondrial isoform 1 (human) def: "An isovaleryl-CoA dehydrogenase, mitochondrial isoform 1 that is encoded in the genome of human." [PMID:1310317] comment: Category=organism-sequence. synonym: "hIVD/iso:1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:P26440-1 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000025738 ! isovaleryl-CoA dehydrogenase, mitochondrial isoform 1 [Term] id: PR:P26440-2 name: isovaleryl-CoA dehydrogenase, mitochondrial isoform h2 (human) def: "An isovaleryl-CoA dehydrogenase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P26440-2." [PRO:DNx, UniProtKB:P26440] comment: Category=organism-sequence. synonym: "hIVD/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:P26440-2 is_a: PR:P26440 ! isovaleryl-CoA dehydrogenase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:P26440 name: isovaleryl-CoA dehydrogenase, mitochondrial (human) def: "An isovaleryl-CoA dehydrogenase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P26440] comment: Category=organism-gene. synonym: "IVD" RELATED Gene-based [UniProtKB:P26440] synonym: "hIVD" EXACT PRO-short-label [PRO:DNx] synonym: "butyryl-CoA dehydrogenase (human)" RELATED [UniProtKB:P26440] xref: UniProtKB:P26440 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000009166 ! isovaleryl-CoA dehydrogenase, mitochondrial relationship: has_gene_template HGNC:6186 ! IVD (human) [Term] id: PR:Q9JHI5 name: isovaleryl-CoA dehydrogenase, mitochondrial (mouse) def: "An isovaleryl-CoA dehydrogenase, mitochondrial that is encoded in the genome of mouse." [PRO:DNx] comment: Category=organism-gene. synonym: "Ivd" RELATED Gene-based [UniProtKB:Q9JHI5] synonym: "mIVD" EXACT PRO-short-label [PRO:DNx] synonym: "IVD (mouse)" EXACT [UniProtKB:Q9JHI5] synonym: "butyryl-CoA dehydrogenase (mouse)" RELATED [UniProtKB:Q9JHI5] xref: UniProtKB:Q9JHI5 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000009166 ! isovaleryl-CoA dehydrogenase, mitochondrial relationship: has_gene_template MGI:1929242 ! Ivd (mouse) [Term] id: PR:Q9SWG0 name: isovaleryl-CoA dehydrogenase, mitochondrial (Arabidopsis thaliana) def: "An isovaleryl-CoA dehydrogenase, mitochondrial that is encoded in the genome of Arabidopsis thaliana." [PRO:DNx] comment: Category=organism-gene. synonym: "IVD" RELATED Gene-based [UniProtKB:Q9SWG0] synonym: "At-IVD" EXACT PRO-short-label [PRO:DNx] synonym: "F18N11.6" RELATED Gene-based [UniProtKB:Q9SWG0] synonym: "At3g45300" RELATED Gene-based [UniProtKB:Q9SWG0] xref: UniProtKB:Q9SWG0 intersection_of: only_in_taxon NCBITaxon:3702 ! Arabidopsis thaliana intersection_of: PR:000009166 ! isovaleryl-CoA dehydrogenase, mitochondrial relationship: has_gene_template Araport:AT3G45300 ! IVD (Arabidopsis thaliana) [Term] id: PR:P12007 name: isovaleryl-CoA dehydrogenase, mitochondrial (rat) def: "An isovaleryl-CoA dehydrogenase, mitochondrial that is encoded in the genome of rat." [PANTHER:PTHR10909:SF121, PRO:DNx] comment: Category=organism-gene. synonym: "Ivd" RELATED Gene-based [UniProtKB:P12007] synonym: "rIVD" EXACT PRO-short-label [PRO:DNx] synonym: "IVD (rat)" EXACT [UniProtKB:P12007] synonym: "butyryl-CoA dehydrogenase (rat)" RELATED [UniProtKB:P12007] xref: UniProtKB:P12007 intersection_of: only_in_taxon NCBITaxon:10116 ! Rattus norvegicus intersection_of: PR:000009166 ! isovaleryl-CoA dehydrogenase, mitochondrial relationship: has_gene_template RGD:2936 ! Ivd (rat) [Term] id: PR:Q9JHI5-1 name: isovaleryl-CoA dehydrogenase, mitochondrial isoform 1 (mouse) def: "An isovaleryl-CoA dehydrogenase, mitochondrial isoform 1 that is encoded in the genome of mouse." [PMID:11404023, PRO:HJD] comment: Category=organism-sequence. synonym: "mIVD/iso:1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q9JHI5-1 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000025738 ! isovaleryl-CoA dehydrogenase, mitochondrial isoform 1