[Term] id: PR:Q54RA2 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (Dictyostelium discoideum) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial that is encoded in the genome of Dictyostelium discoideum." [OMA:Q54RA2, PRO:DNx] comment: Category=organism-gene. synonym: "DDB_G0283293" RELATED Gene-based [UniProtKB:Q54RA2] synonym: "Dicty-ALDH4A1" EXACT PRO-short-label [PRO:DNx] synonym: "P5C dehydrogenase (Dictyostelium discoideum)" EXACT [UniProtKB:Q54RA2] synonym: "L-glutamate gamma-semialdehyde dehydrogenase (Dictyostelium discoideum)" EXACT [UniProtKB:Q54RA2] synonym: "aldehyde dehydrogenase family 4 member A1 homolog (Dictyostelium discoideum)" EXACT [UniProtKB:Q54RA2] xref: UniProtKB:Q54RA2 intersection_of: only_in_taxon NCBITaxon:44689 ! Dictyostelium discoideum intersection_of: PR:000003928 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial relationship: has_gene_template dictyBase:DDB_G0283293 ! DDB_G0283293 (Dictyostelium discoideum) [Term] id: PR:Q7SY23 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (zebrafish) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial that is encoded in the genome of zebrafish." [OMA:Q7SY23, PRO:DNx] comment: Category=organism-gene. synonym: "aldh4a1" RELATED Gene-based [UniProtKB:Q7SY23] synonym: "z-ALDH4A1" EXACT PRO-short-label [PRO:DNx] synonym: "zgc:63592" RELATED Gene-based [UniProtKB:Q7SY23] synonym: "P5C dehydrogenase (zebrafish)" EXACT [UniProtKB:Q7SY23] synonym: "aldehyde dehydrogenase family 4 member A1 (zebrafish)" EXACT [UniProtKB:Q7SY23] synonym: "L-glutamate gamma-semialdehyde dehydrogenase (zebrafish)" EXACT [UniProtKB:Q7SY23] xref: UniProtKB:Q7SY23 intersection_of: only_in_taxon NCBITaxon:7955 ! Danio rerio intersection_of: PR:000003928 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial relationship: has_gene_template ZFIN:ZDB-GENE-040426-1179 ! aldh4a1 (zebrafish) [Term] id: PR:Q8CHT0 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (mouse) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial that is encoded in the genome of mouse." [OMA:Q8CHT0, PRO:DNx] comment: Category=organism-gene. synonym: "Aldh4a1" RELATED Gene-based [UniProtKB:Q8CHT0] synonym: "mALDH4A1" EXACT PRO-short-label [PRO:DNx] synonym: "P5C dehydrogenase (mouse)" EXACT [UniProtKB:Q8CHT0] synonym: "aldehyde dehydrogenase family 4 member A1 (mouse)" EXACT [UniProtKB:Q8CHT0] synonym: "L-glutamate gamma-semialdehyde dehydrogenase (mouse)" EXACT [UniProtKB:Q8CHT0] xref: UniProtKB:Q8CHT0 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000003928 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial relationship: has_gene_template MGI:2443883 ! Aldh4a1 (mouse) [Term] id: PR:P07275 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (yeast) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial that is encoded in the genome of yeast." [OMA:P07275, PRO:DNx] comment: Category=organism-gene. synonym: "PUT2" RELATED Gene-based [UniProtKB:P07275] synonym: "YHR037W" RELATED Gene-based [UniProtKB:P07275] synonym: "yALDH4A1" EXACT PRO-short-label [PRO:DNx] synonym: "P5C dehydrogenase (yeast)" EXACT [UniProtKB:P07275] synonym: "L-glutamate gamma-semialdehyde dehydrogenase (yeast)" EXACT [UniProtKB:P07275] xref: UniProtKB:P07275 intersection_of: only_in_taxon NCBITaxon:559292 ! Saccharomyces cerevisiae S288C intersection_of: PR:000003928 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial relationship: has_gene_template SGD:S000001079 ! PUT2 (yeast) [Term] id: PR:P30038-2 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform h2 (human) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P30038-2." [PRO:DNx, UniProtKB:P30038] comment: Category=organism-sequence. synonym: "hALDH4A1/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:P30038-2 is_a: PR:P30038 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:P30038-3 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform h3 (human) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P30038-3." [PRO:DNx, UniProtKB:P30038] comment: Category=organism-sequence. synonym: "hALDH4A1/iso:h3" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:P30038-3 is_a: PR:P30038 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:P30038 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P30038] comment: Category=organism-gene. synonym: "ALDH4" RELATED Gene-based [UniProtKB:P30038] synonym: "P5CDH" RELATED Gene-based [UniProtKB:P30038] synonym: "ALDH4A1" RELATED Gene-based [UniProtKB:P30038] synonym: "hALDH4A1" EXACT PRO-short-label [PRO:DNx] synonym: "P5C dehydrogenase (human)" EXACT [UniProtKB:P30038] synonym: "aldehyde dehydrogenase family 4 member A1 (human)" EXACT [UniProtKB:P30038] synonym: "L-glutamate gamma-semialdehyde dehydrogenase (human)" EXACT [UniProtKB:P30038] xref: UniProtKB:P30038 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000003928 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial relationship: has_gene_template HGNC:406 ! ALDH4A1 (human) [Term] id: PR:O74766 name: probable delta-1-pyrroline-5-carboxylate dehydrogenase (Schizosaccharomyces pombe 972h-) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial that is encoded in the genome of Schizosaccharomyces pombe 972h-." [OMA:O74766, PRO:DNx] comment: Category=organism-gene. synonym: "SPBC24C6.04" RELATED Gene-based [UniProtKB:O74766] synonym: "Spom972h-ALDH4A1" EXACT PRO-short-label [PRO:DNx] synonym: "P5C dehydrogenase (Schizosaccharomyces pombe 972h-)" EXACT [UniProtKB:O74766] synonym: "L-glutamate gamma-semialdehyde dehydrogenase (Schizosaccharomyces pombe 972h-)" EXACT [UniProtKB:O74766] xref: UniProtKB:O74766 intersection_of: only_in_taxon NCBITaxon:284812 ! Schizosaccharomyces pombe 972h- intersection_of: PR:000003928 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial relationship: has_gene_template PomBase:SPBC24C6.04 ! SPBC24C6.04 (Schizosaccharomyces pombe) [Term] id: PR:000003928 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial def: "A protein that is a translation product of the human ALDH4A1 gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "ALDH4" RELATED Gene-based [] synonym: "P5CDH" RELATED Gene-based [] synonym: "ALDH4A1" EXACT PRO-short-label [PRO:DNx] synonym: "P5C dehydrogenase" EXACT [] synonym: "aldehyde dehydrogenase family 4 member A1" EXACT [] synonym: "L-glutamate gamma-semialdehyde dehydrogenase" EXACT [] is_a: PR:000000001 ! protein [Term] id: PR:000046313 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial, transit peptide removed form (human) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) that has had the transit peptide removed. UniProtKB:P30038, 25-563." [PRO:DNx, Reactome:R-HSA-70673] comment: Category=organism-modification. synonym: "PRO_0000007173" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hALDH4A1/TransPep-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:P30038, 25-563" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-70673 "PR:000046313 located_in GO:0005759" intersection_of: PR:P30038 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) intersection_of: lacks_part SO:0000725 ! transit_peptide relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:P30038-1 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform h1 (human) def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P30038-1." [PRO:DNx, UniProtKB:P30038] comment: Category=organism-sequence. synonym: "hALDH4A1/iso:h1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:P30038-1 is_a: PR:P30038 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:000018956 name: delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial, transit peptide removed form def: "A delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial that has had the transit peptide removed." [PRO:DNx] comment: Category=modification. synonym: "ALDH4A1/TransPep-" EXACT PRO-short-label [PRO:DNx] intersection_of: PR:000003928 ! delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial intersection_of: lacks_part SO:0000725 ! transit_peptide