[Term] id: PR:P12694 name: 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (human) def: "A 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P12694] comment: Category=organism-gene. synonym: "BCKDHA" RELATED Gene-based [UniProtKB:P12694] synonym: "hBCKDHA" EXACT PRO-short-label [PRO:DNx] synonym: "BCKDE1A (human)" EXACT [UniProtKB:P12694] synonym: "BCKDH E1-alpha (human)" EXACT [UniProtKB:P12694] synonym: "branched-chain alpha-keto acid dehydrogenase E1 component alpha chain (human)" EXACT [UniProtKB:P12694] xref: UniProtKB:P12694 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000004686 ! 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial relationship: has_gene_template HGNC:986 ! BCKDHA (human)