[Term] id: PR:O00330-3 name: pyruvate dehydrogenase protein X component, mitochondrial isoform h3 (human) def: "A pyruvate dehydrogenase protein X component, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:O00330-3." [PRO:DNx, UniProtKB:O00330] comment: Category=organism-sequence. synonym: "hPDHX/iso:h3" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:O00330-3 is_a: PR:O00330 ! pyruvate dehydrogenase protein X component, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:O00330-2 name: pyruvate dehydrogenase protein X component, mitochondrial isoform h2 (human) def: "A pyruvate dehydrogenase protein X component, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:O00330-2." [PRO:DNx, UniProtKB:O00330] comment: Category=organism-sequence. synonym: "hPDHX/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:O00330-2 is_a: PR:O00330 ! pyruvate dehydrogenase protein X component, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:O00330-1 name: pyruvate dehydrogenase protein X component, mitochondrial isoform h1 (human) def: "A pyruvate dehydrogenase protein X component, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:O00330-1." [PRO:DNx, UniProtKB:O00330] comment: Category=organism-sequence. synonym: "hPDHX/iso:h1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:O00330-1 is_a: PR:O00330 ! pyruvate dehydrogenase protein X component, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:000012496 name: pyruvate dehydrogenase protein X component, mitochondrial def: "A protein that is a translation product of the human PDHX gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "E3BP" EXACT [] synonym: "PDHX" EXACT PRO-short-label [PRO:DNx] synonym: "PDX1" RELATED Gene-based [] synonym: "proX" BROAD [PRO:DNx] synonym: "E3-binding protein" EXACT [] synonym: "lipoyl-containing pyruvate dehydrogenase complex component X" EXACT [] synonym: "dihydrolipoamide dehydrogenase-binding protein of pyruvate dehydrogenase complex" EXACT [] is_a: PR:000000001 ! protein [Term] id: PR:000048728 name: pyruvate dehydrogenase protein X component, mitochondrial, transit peptide removed form (human) def: "A pyruvate dehydrogenase protein X component, mitochondrial (human) that has had the transit peptide removed. UniProtKB:O00330, 54-501." [PRO:DNx, Reactome:R-HSA-70059] comment: Category=organism-modification. synonym: "PRO_0000020484" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hPDHX/TransPep-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:O00330, 54-501" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-70059 "PR:000048728 located_in GO:0005759" intersection_of: PR:O00330 ! pyruvate dehydrogenase protein X component, mitochondrial (human) intersection_of: lacks_part SO:0000725 ! transit_peptide relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:O00330 name: pyruvate dehydrogenase protein X component, mitochondrial (human) def: "A pyruvate dehydrogenase protein X component, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:O00330] comment: Category=organism-gene. synonym: "PDHX" RELATED Gene-based [UniProtKB:O00330] synonym: "PDX1" RELATED Gene-based [UniProtKB:O00330] synonym: "hPDHX" EXACT PRO-short-label [PRO:DNx] synonym: "E3BP (human)" EXACT [UniProtKB:O00330] synonym: "proX (human)" EXACT [UniProtKB:O00330] synonym: "E3-binding protein (human)" EXACT [UniProtKB:O00330] synonym: "lipoyl-containing pyruvate dehydrogenase complex component X (human)" EXACT [UniProtKB:O00330] synonym: "dihydrolipoamide dehydrogenase-binding protein of pyruvate dehydrogenase complex (human)" EXACT [UniProtKB:O00330] xref: UniProtKB:O00330 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000012496 ! pyruvate dehydrogenase protein X component, mitochondrial relationship: has_gene_template HGNC:21350 ! PDHX (human)