[Term] id: PR:000048603 name: peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase, initiator methionine removed form (human) def: "A peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) that has had the initiator methionine removed. UniProtKB:Q96IV0, 2-654." [PRO:DNx, Reactome:R-HSA-8850591] comment: Category=organism-modification. synonym: "PRO_0000248971" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hNGLY1/InitMet-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:Q96IV0, 2-654" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-8850591 "PR:000048603 located_in GO:0005829" intersection_of: lacks_part PR:000021937 ! initiator methionine intersection_of: PR:Q96IV0 ! peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q96IV0 name: peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) def: "A peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase that is encoded in the genome of human." [PRO:DNx, UniProtKB:Q96IV0] comment: Category=organism-gene. synonym: "PNG1" RELATED Gene-based [UniProtKB:Q96IV0] synonym: "NGLY1" RELATED Gene-based [UniProtKB:Q96IV0] synonym: "hNGLY1" EXACT PRO-short-label [PRO:DNx] synonym: "hPNGase" EXACT [UniProtKB:Q96IV0] synonym: "PNGase (human)" EXACT [UniProtKB:Q96IV0] synonym: "N-glycanase 1 (human)" EXACT [UniProtKB:Q96IV0] synonym: "peptide:N-glycanase (human)" EXACT [UniProtKB:Q96IV0] xref: UniProtKB:Q96IV0 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000011196 ! peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase relationship: has_gene_template HGNC:17646 ! NGLY1 (human) [Term] id: PR:000011196 name: peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase def: "A protein that is a translation product of the human NGLY1 gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "PNG1" RELATED Gene-based [] synonym: "NGLY1" EXACT PRO-short-label [PRO:DNx] synonym: "PNGase" EXACT [] synonym: "N-glycanase 1" EXACT [] synonym: "peptide:N-glycanase" EXACT [] is_a: PR:000000001 ! protein [Term] id: PR:Q96IV0-5 name: peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase isoform h5 (human) def: "A peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q96IV0-5." [PRO:DNx, UniProtKB:Q96IV0] comment: Category=organism-sequence. synonym: "hNGLY1/iso:h5" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q96IV0-5 is_a: PR:Q96IV0 ! peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q96IV0-4 name: peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase isoform h4 (human) def: "A peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q96IV0-4." [PRO:DNx, UniProtKB:Q96IV0] comment: Category=organism-sequence. synonym: "hNGLY1/iso:h4" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q96IV0-4 is_a: PR:Q96IV0 ! peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q96IV0-3 name: peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase isoform h3 (human) def: "A peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q96IV0-3." [PRO:DNx, UniProtKB:Q96IV0] comment: Category=organism-sequence. synonym: "hNGLY1/iso:h3" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q96IV0-3 is_a: PR:Q96IV0 ! peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q96IV0-2 name: peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase isoform h2 (human) def: "A peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q96IV0-2." [PRO:DNx, UniProtKB:Q96IV0] comment: Category=organism-sequence. synonym: "hNGLY1/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q96IV0-2 is_a: PR:Q96IV0 ! peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q96IV0-1 name: peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase isoform h1 (human) def: "A peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q96IV0-1." [PRO:DNx, UniProtKB:Q96IV0] comment: Category=organism-sequence. synonym: "hNGLY1/iso:h1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q96IV0-1 is_a: PR:Q96IV0 ! peptide-N(4)-(N-acetyl-beta-glucosaminyl)asparagine amidase (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens