[Term] id: PR:P07896 name: peroxisomal bifunctional enzyme (rat) def: "A peroxisomal bifunctional enzyme that is encoded in the genome of rat." [OMA:P07896, PRO:DNx] comment: Category=organism-gene. synonym: "Mfe1" RELATED Gene-based [UniProtKB:P07896] synonym: "Ehhadh" RELATED Gene-based [UniProtKB:P07896] synonym: "rEHHADH" EXACT PRO-short-label [PRO:DNx] synonym: "PBE (rat)" EXACT [UniProtKB:P07896] synonym: "MFE1 (rat)" EXACT [UniProtKB:P07896] synonym: "MFP1 (rat)" EXACT [UniProtKB:P07896] synonym: "PBFE (rat)" EXACT [UniProtKB:P07896] synonym: "multifunctional enzyme 1 (rat)" EXACT [UniProtKB:P07896] synonym: "multifunctional protein 1 (rat)" EXACT [UniProtKB:P07896] xref: UniProtKB:P07896 intersection_of: only_in_taxon NCBITaxon:10116 ! Rattus norvegicus intersection_of: PR:000006947 ! peroxisomal bifunctional enzyme relationship: has_gene_template RGD:621441 ! Ehhadh (rat) [Term] id: PR:000006947 name: peroxisomal bifunctional enzyme def: "A protein that is a translation product of the human EHHADH gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "PBE" EXACT [] synonym: "ECHD" RELATED Gene-based [] synonym: "MFE1" EXACT [] synonym: "PBFE" EXACT [] synonym: "EHHADH" EXACT PRO-short-label [PRO:DNx] synonym: "multifunctional enzyme 1" EXACT [] is_a: PR:000000001 ! protein [Term] id: PR:Q08426-2 name: peroxisomal bifunctional enzyme isoform h2 (human) def: "A peroxisomal bifunctional enzyme (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q08426-2." [PRO:DNx, UniProtKB:Q08426] comment: Category=organism-sequence. synonym: "hEHHADH/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q08426-2 is_a: PR:Q08426 ! peroxisomal bifunctional enzyme (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q08426-1 name: peroxisomal bifunctional enzyme isoform h1 (human) def: "A peroxisomal bifunctional enzyme (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q08426-1." [PRO:DNx, UniProtKB:Q08426] comment: Category=organism-sequence. synonym: "hEHHADH/iso:h1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q08426-1 is_a: PR:Q08426 ! peroxisomal bifunctional enzyme (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q9DBM2 name: peroxisomal bifunctional enzyme (mouse) def: "A peroxisomal bifunctional enzyme that is encoded in the genome of mouse." [OMA:Q9DBM2, PRO:DNx] comment: Category=organism-gene. synonym: "L-pbe" RELATED Gene-based [UniProtKB:Q9DBM2] synonym: "Ehhadh" RELATED Gene-based [UniProtKB:Q9DBM2] synonym: "mEHHADH" EXACT PRO-short-label [PRO:DNx] synonym: "PBE (mouse)" EXACT [UniProtKB:Q9DBM2] synonym: "MFE1 (mouse)" EXACT [UniProtKB:Q9DBM2] synonym: "PBFE (mouse)" EXACT [UniProtKB:Q9DBM2] synonym: "L-PBE (mouse)" EXACT [UniProtKB:Q9DBM2] synonym: "MFP-1 (mouse)" EXACT [UniProtKB:Q9DBM2] synonym: "multifunctional enzyme 1 (mouse)" EXACT [UniProtKB:Q9DBM2] synonym: "multifunctional protein 1 (mouse)" EXACT [UniProtKB:Q9DBM2] synonym: "L-peroxisomal bifunctional enzyme (mouse)" EXACT [UniProtKB:Q9DBM2] xref: UniProtKB:Q9DBM2 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000006947 ! peroxisomal bifunctional enzyme relationship: has_gene_template MGI:1277964 ! Ehhadh (mouse) [Term] id: PR:Q6NYL3 name: peroxisomal bifunctional enzyme (zebrafish) def: "A peroxisomal bifunctional enzyme that is encoded in the genome of zebrafish." [OMA:Q6NYL3, PRO:DNx] comment: Category=organism-gene. synonym: "echd" RELATED Gene-based [UniProtKB:Q6NYL3] synonym: "ehhadh" RELATED Gene-based [UniProtKB:Q6NYL3] synonym: "z-EHHADH" EXACT PRO-short-label [PRO:DNx] synonym: "zgc:77526" RELATED Gene-based [UniProtKB:Q6NYL3] synonym: "PBE (zebrafish)" EXACT [UniProtKB:Q6NYL3] synonym: "si:dkeyp-30d5.2" RELATED Gene-based [UniProtKB:Q6NYL3] synonym: "MFE1 (zebrafish)" EXACT [UniProtKB:Q6NYL3] synonym: "PBFE (zebrafish)" EXACT [UniProtKB:Q6NYL3] synonym: "multifunctional enzyme 1 (zebrafish)" EXACT [UniProtKB:Q6NYL3] xref: UniProtKB:Q6NYL3 intersection_of: only_in_taxon NCBITaxon:7955 ! Danio rerio intersection_of: PR:000006947 ! peroxisomal bifunctional enzyme relationship: has_gene_template ZFIN:ZDB-GENE-040426-2581 ! ehhadh (zebrafish) [Term] id: PR:Q08426 name: peroxisomal bifunctional enzyme (human) def: "A peroxisomal bifunctional enzyme that is encoded in the genome of human." [PRO:DNx, UniProtKB:Q08426] comment: Category=organism-gene. synonym: "ECHD" RELATED Gene-based [UniProtKB:Q08426] synonym: "EHHADH" RELATED Gene-based [UniProtKB:Q08426] synonym: "hEHHADH" EXACT PRO-short-label [PRO:DNx] synonym: "LBP (human)" RELATED [UniProtKB:Q08426] synonym: "PBE (human)" EXACT [UniProtKB:Q08426] synonym: "MFE1 (human)" EXACT [UniProtKB:Q08426] synonym: "PBFE (human)" EXACT [UniProtKB:Q08426] synonym: "L-bifunctional protein (human)" EXACT [UniProtKB:Q08426] synonym: "multifunctional enzyme 1 (human)" EXACT [UniProtKB:Q08426] xref: Reactome:R-HSA-400155 "PR:Q08426 located_in GO:0005782" xref: Reactome:R-HSA-9033147 "PR:Q08426 located_in GO:0005829" xref: UniProtKB:Q08426 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000006947 ! peroxisomal bifunctional enzyme relationship: has_gene_template HGNC:3247 ! EHHADH (human)