[Term] id: PR:000006300 name: lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial def: "A protein that is a translation product of the human DBT gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "DBT" EXACT PRO-short-label [PRO:DNx] synonym: "BCATE2" RELATED Gene-based [] synonym: "BCKADE2" EXACT [] synonym: "BCKAD-E2" EXACT [] synonym: "dihydrolipoamide branched chain transacylase" EXACT [] synonym: "dihydrolipoyllysine-residue (2-methylpropanoyl)transferase" EXACT [] synonym: "branched-chain alpha-keto acid dehydrogenase complex component E2" EXACT [] synonym: "dihydrolipoamide acetyltransferase component of branched-chain alpha-keto acid dehydrogenase complex" EXACT [] is_a: PR:000000001 ! protein