[Term]
id: PR:000046472
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, transit peptide removed form (human)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that has had the transit peptide removed. UniProtKB:P21953, 51-392." [PRO:DNx, Reactome:R-HSA-70015]
comment: Category=organism-modification.
synonym: "PRO_0000020470" EXACT PRO-proteoform-ftid [PRO:DNx]
synonym: "hBCKDHB/TransPep-" EXACT PRO-short-label [PRO:DNx]
synonym: "UniProtKB:P21953, 51-392" EXACT PRO-proteoform-std [PRO:DNx]
xref: Reactome:R-HSA-70015 "PR:000046472 located_in GO:0005759"
intersection_of: PR:P21953 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human)
intersection_of: lacks_part SO:0000725 ! transit_peptide
relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens

[Term]
id: PR:000041193
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform 1
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q6P3A8-1 or a 1:1 ortholog thereof." [PRO:DNx]
comment: Category=sequence.
synonym: "BCKDHB/iso:1" EXACT PRO-short-label [PRO:DNx]
is_a: PR:000004687 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial

[Term]
id: PR:Q6P3A8
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (mouse)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is encoded in the genome of mouse." [OMA:Q6P3A8, PRO:DNx]
comment: Category=organism-gene.
synonym: "Bckdhb" RELATED Gene-based [UniProtKB:Q6P3A8]
synonym: "mBCKDHB" EXACT PRO-short-label [PRO:DNx]
synonym: "BCKDE1B (mouse)" EXACT [UniProtKB:Q6P3A8]
synonym: "BCKDH E1-beta (mouse)" EXACT [UniProtKB:Q6P3A8]
synonym: "branched-chain alpha-keto acid dehydrogenase E1 component beta chain (mouse)" EXACT [UniProtKB:Q6P3A8]
xref: UniProtKB:Q6P3A8
intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus
intersection_of: PR:000004687 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
relationship: has_gene_template MGI:88137 ! Bckdhb (mouse)

[Term]
id: PR:Q6P3A8-2
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform m2 (mouse)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (mouse) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q6P3A8-2." [PRO:DNx, UniProtKB:Q6P3A8]
comment: Category=organism-sequence.
synonym: "mBCKDHB/iso:m2" EXACT PRO-short-label [PRO:DNx]
xref: UniProtKB:Q6P3A8-2
is_a: PR:Q6P3A8 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (mouse)
relationship: only_in_taxon NCBITaxon:10090 ! Mus musculus

[Term]
id: PR:Q6P3A8-1
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform 1 (mouse)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform 1 that is encoded in the genome of mouse." [PRO:DNx]
comment: Category=organism-sequence.
synonym: "mBCKDHB/iso:1" EXACT PRO-short-label [PRO:DNx]
xref: UniProtKB:Q6P3A8-1
intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus
intersection_of: PR:000041193 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform 1

[Term]
id: PR:P35738
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (rat)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is encoded in the genome of rat." [OMA:P35738, PRO:DNx]
comment: Category=organism-gene.
synonym: "Bckdhb" RELATED Gene-based [UniProtKB:P35738]
synonym: "rBCKDHB" EXACT PRO-short-label [PRO:DNx]
synonym: "BCKDE1B (rat)" EXACT [UniProtKB:P35738]
synonym: "BCKDH E1-beta (rat)" EXACT [UniProtKB:P35738]
synonym: "branched-chain alpha-keto acid dehydrogenase E1 component beta chain (rat)" EXACT [UniProtKB:P35738]
xref: UniProtKB:P35738
intersection_of: only_in_taxon NCBITaxon:10116 ! Rattus norvegicus
intersection_of: PR:000004687 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
relationship: has_gene_template RGD:2197 ! Bckdhb (rat)

[Term]
id: PR:P21953
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P21953]
comment: Category=organism-gene.
synonym: "BCKDHB" RELATED Gene-based [UniProtKB:P21953]
synonym: "hBCKDHB" EXACT PRO-short-label [PRO:DNx]
synonym: "BCKDE1B (human)" EXACT [UniProtKB:P21953]
synonym: "BCKDH E1-beta (human)" EXACT [UniProtKB:P21953]
synonym: "branched-chain alpha-keto acid dehydrogenase E1 component beta chain (human)" EXACT [UniProtKB:P21953]
xref: UniProtKB:P21953
intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens
intersection_of: PR:000004687 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
relationship: has_gene_template HGNC:987 ! BCKDHB (human)

[Term]
id: PR:000019129
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, transit peptide removed form
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that has had the transit peptide removed." [PRO:DNx]
comment: Category=modification.
synonym: "BCKDHB/TransPep-" EXACT PRO-short-label [PRO:DNx]
intersection_of: PR:000004687 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
intersection_of: lacks_part SO:0000725 ! transit_peptide

[Term]
id: PR:P21953-1
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform h1 (human)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P21953-1." [PRO:DNx, UniProtKB:P21953]
comment: Category=organism-sequence.
synonym: "hBCKDHB/iso:h1" EXACT PRO-short-label [PRO:DNx]
xref: UniProtKB:P21953-1
is_a: PR:P21953 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human)
relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens

[Term]
id: PR:P21953-2
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform h2 (human)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P21953-2." [PRO:DNx, UniProtKB:P21953]
comment: Category=organism-sequence.
synonym: "hBCKDHB/iso:h2" EXACT PRO-short-label [PRO:DNx]
xref: UniProtKB:P21953-2
is_a: PR:P21953 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human)
relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens

[Term]
id: PR:P35738-1
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform 1 (rat)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform 1 that is encoded in the genome of rat." [PRO:DNx]
comment: Category=organism-sequence.
synonym: "rBCKDHB/iso:1" EXACT PRO-short-label [PRO:DNx]
xref: UniProtKB:P35738-1
intersection_of: only_in_taxon NCBITaxon:10116 ! Rattus norvegicus
intersection_of: PR:000041193 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform 1

[Term]
id: PR:000004687
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
def: "A protein that is a translation product of the human BCKDHB gene or a 1:1 ortholog thereof." [PRO:DNx]
comment: Category=gene.
synonym: "BCKDHB" EXACT PRO-short-label [PRO:DNx]
synonym: "BCKDE1B" EXACT []
synonym: "BCKDH E1-beta" EXACT []
synonym: "branched-chain alpha-keto acid dehydrogenase E1 component beta chain" EXACT []
is_a: PR:000000001 ! protein

[Term]
id: PR:Q55FN7
name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (Dictyostelium discoideum)
def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is encoded in the genome of Dictyostelium discoideum." [OMA:Q55FN7, PANTHER:PTHR11624:SF21, PRO:DNx]
comment: Category=organism-gene.
synonym: "bkdB" RELATED Gene-based [UniProtKB:Q55FN7]
synonym: "DDB_G0268020" RELATED Gene-based [UniProtKB:Q55FN7]
synonym: "Dicty-BCKDHB" EXACT PRO-short-label [PRO:DNx]
synonym: "BCKDE1B (Dictyostelium discoideum)" EXACT [UniProtKB:Q55FN7]
synonym: "BCKDH E1-beta (Dictyostelium discoideum)" EXACT [UniProtKB:Q55FN7]
synonym: "3-methyl-2-oxobutanoate dehydrogenase (Dictyostelium discoideum)" EXACT [UniProtKB:Q55FN7]
synonym: "branched-chain alpha-keto acid dehydrogenase E1 component beta chain (Dictyostelium discoideum)" EXACT [UniProtKB:Q55FN7]
xref: UniProtKB:Q55FN7
intersection_of: only_in_taxon NCBITaxon:44689 ! Dictyostelium discoideum
intersection_of: PR:000004687 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
relationship: has_gene_template dictyBase:DDB_G0268020 ! bkdB (Dictyostelium discoideum)