[Term] id: PR:000004686 name: 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial def: "A protein that is a translation product of the human BCKDHA gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "BCKDHA" EXACT PRO-short-label [PRO:DNx] synonym: "BCKDE1A" EXACT [] synonym: "BCKDH E1-alpha" EXACT [] synonym: "branched-chain alpha-keto acid dehydrogenase E1 component alpha chain" EXACT [] is_a: PR:000000001 ! protein