[Term]
id: PR:000003632
name: aconitate hydratase, mitochondrial
def: "A protein that is a translation product of the human ACO2 gene or a 1:1 ortholog thereof." [PRO:DNx]
comment: Category=gene.
synonym: "ACO2" EXACT PRO-short-label [PRO:DNx]
synonym: "aconitase" BROAD [PRO:DNx]
synonym: "citrate hydro-lyase" BROAD [PRO:DNx]
is_a: PR:000000001 ! protein

[Term]
id: PR:000046240
name: aconitate hydratase, mitochondrial, transit peptide removed form (human)
def: "An aconitate hydratase, mitochondrial (human) that has had the transit peptide removed. UniProtKB:Q99798, 28-780." [PRO:DNx, Reactome:R-HSA-70968]
comment: Category=organism-modification.
synonym: "PRO_0000000541" EXACT PRO-proteoform-ftid [PRO:DNx]
synonym: "hACO2/TransPep-" EXACT PRO-short-label [PRO:DNx]
synonym: "UniProtKB:Q99798, 28-780" EXACT PRO-proteoform-std [PRO:DNx]
xref: Reactome:R-HSA-70968 "PR:000046240 located_in GO:0005759"
intersection_of: PR:Q99798 ! aconitate hydratase, mitochondrial (human)
intersection_of: lacks_part SO:0000725 ! transit_peptide
relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens

[Term]
id: PR:Q99798
name: aconitate hydratase, mitochondrial (human)
def: "An aconitate hydratase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:Q99798]
comment: Category=organism-gene.
synonym: "ACO2" RELATED Gene-based [UniProtKB:Q99798]
synonym: "hACO2" EXACT PRO-short-label [PRO:DNx]
synonym: "aconitase (human)" BROAD [UniProtKB:Q99798]
synonym: "citrate hydro-lyase (human)" BROAD [UniProtKB:Q99798]
xref: UniProtKB:Q99798
xref: Reactome:R-HSA-1267957 "PR:Q99798 located_in GO:0005758"
xref: Reactome:R-HSA-1267965 "PR:Q99798 located_in GO:0005829"
intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens
intersection_of: PR:000003632 ! aconitate hydratase, mitochondrial
relationship: has_gene_template HGNC:118 ! ACO2 (human)

[Term]
id: PR:Q99798-1
name: aconitate hydratase, mitochondrial isoform 1 (human)
def: "An aconitate hydratase, mitochondrial isoform 1 that is encoded in the genome of human." [PRO:DNx]
comment: Category=organism-sequence.
synonym: "hACO2/iso:1" EXACT PRO-short-label [PRO:DNx]
xref: UniProtKB:Q99798-1
intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens
intersection_of: PR:000042747 ! aconitate hydratase, mitochondrial isoform 1