[Term] id: PR:Q9UKU7-2 name: isobutyryl-CoA dehydrogenase, mitochondrial isoform h2 (human) def: "An isobutyryl-CoA dehydrogenase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q9UKU7-2." [PRO:DNx, UniProtKB:Q9UKU7] comment: Category=organism-sequence. synonym: "hACAD8/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q9UKU7-2 is_a: PR:Q9UKU7 ! isobutyryl-CoA dehydrogenase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q9UKU7-3 name: isobutyryl-CoA dehydrogenase, mitochondrial isoform h3 (human) def: "An isobutyryl-CoA dehydrogenase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q9UKU7-3." [PRO:DNx, UniProtKB:Q9UKU7] comment: Category=organism-sequence. synonym: "hACAD8/iso:h3" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q9UKU7-3 is_a: PR:Q9UKU7 ! isobutyryl-CoA dehydrogenase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q9UKU7-1 name: isobutyryl-CoA dehydrogenase, mitochondrial isoform h1 (human) def: "An isobutyryl-CoA dehydrogenase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q9UKU7-1." [PRO:DNx, UniProtKB:Q9UKU7] comment: Category=organism-sequence. synonym: "hACAD8/iso:h1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q9UKU7-1 is_a: PR:Q9UKU7 ! isobutyryl-CoA dehydrogenase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q9UKU7 name: isobutyryl-CoA dehydrogenase, mitochondrial (human) def: "An isobutyryl-CoA dehydrogenase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:Q9UKU7] comment: Category=organism-gene. synonym: "IBD" RELATED Gene-based [UniProtKB:Q9UKU7] synonym: "ACAD8" RELATED Gene-based [UniProtKB:Q9UKU7] synonym: "ARC42" RELATED Gene-based [UniProtKB:Q9UKU7] synonym: "hACAD8" EXACT PRO-short-label [PRO:DNx] synonym: "IBDH (human)" EXACT [UniProtKB:Q9UKU7] synonym: "ACAD-8 (human)" EXACT [UniProtKB:Q9UKU7] synonym: "acyl-CoA dehydrogenase family member 8 (human)" EXACT [UniProtKB:Q9UKU7] synonym: "activator-recruited cofactor 42 kDa component (human)" EXACT [UniProtKB:Q9UKU7] xref: UniProtKB:Q9UKU7 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000003598 ! isobutyryl-CoA dehydrogenase, mitochondrial relationship: has_gene_template HGNC:87 ! ACAD8 (human) [Term] id: PR:000046231 name: isobutyryl-CoA dehydrogenase, mitochondrial, transit peptide removed form (human) def: "An isobutyryl-CoA dehydrogenase, mitochondrial (human) that has had the transit peptide removed. UniProtKB:Q9UKU7, 23-415." [PRO:DNx, Reactome:R-HSA-70855] comment: Category=organism-modification. synonym: "PRO_0000000522" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hACAD8/TransPep-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:Q9UKU7, 23-415" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-70855 "PR:000046231 located_in GO:0005759" intersection_of: PR:Q9UKU7 ! isobutyryl-CoA dehydrogenase, mitochondrial (human) intersection_of: lacks_part SO:0000725 ! transit_peptide relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:000003598 name: isobutyryl-CoA dehydrogenase, mitochondrial def: "A protein that is a translation product of the human ACAD8 gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "IBD" RELATED Gene-based [] synonym: "ACAD8" EXACT PRO-short-label [PRO:DNx] synonym: "ARC42" RELATED Gene-based [] synonym: "ACAD-8" EXACT [] synonym: "acyl-CoA dehydrogenase family member 8" EXACT [] synonym: "activator-recruited cofactor 42 kDa component" EXACT [] is_a: PR:000000001 ! protein